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[Devic's optic neuromyelitis and viral hepatitis type A. A paediatric case report]
Z Jouhadi1, I Ouazzani, A Abid
1Service de Pédiatrie Infectieuse, Hôpital d'Enfants. jouhadi@lycos.com
Revue Neurologique
|December 17, 2004
Summary
Devic optic neuromyelitis, a rare condition causing myelitis and optic neuropathy, can be triggered by viral hepatitis A. Early corticosteroid treatment in children may improve vision and motor function, though some deficits may persist.
Area of Science:
- Neurology
- Ophthalmology
- Pediatrics
Background:
- Devic optic neuromyelitis (neuromyelitis optica spectrum disorder) is a rare autoimmune condition characterized by severe transverse myelitis and optic neuropathy.
- Pathogenesis is often linked to demyelinization triggered by preceding bacterial or viral infections.
- Pediatric cases suggest a potentially better prognosis compared to adults.
Observation:
- A case report details an 8-year-old child presenting with flaccid tetraplegia and sudden vision loss.
- Ophthalmologic examination revealed bilateral optic neuritis (neuropapillitis).
- Spinal MRI showed extensive myelitis and arachnoiditis.
Findings:
- Infectious workup identified IgM antibodies for Hepatitis A virus, suggesting a potential trigger.
- The child received corticosteroid treatment.
- Significant recovery of vision and upper limb/trunk motor function was observed.
Implications:
- This case highlights Hepatitis A virus as a possible precipitating factor for Devic optic neuromyelitis in children.
- The findings underscore the importance of early diagnosis and treatment with corticosteroids in pediatric cases.
- Further research into infectious triggers and long-term outcomes in pediatric neuromyelitis optica spectrum disorder is warranted.