Enteritis cystica profunda presenting as ileoileal intussusception in a child: report of a case

Hiroki Sunagawa1, Tsukasa Kinjyou, Masayoshi Nagahama

  • 1First Department of Surgery, Faculty of Medicine, University of the Ryukyus, 207 Uehara, Nishihara-cho, Okinawa, 903-0215, Japan.

Surgery Today
|January 28, 2005
PubMed

Insights

This case report details a rare instance of small bowel intussusception in an infant, caused by enteritis cystica profunda (ECP). This condition, leading to intussusception, is exceptionally uncommon in pediatric patients.

Area of Science:

  • Pediatric Surgery
  • Gastroenterology
  • Pathology

Background:

  • Small bowel intussusception is a common surgical emergency in infants.
  • Enteritis cystica profunda (ECP) is a rare benign cystic lesion of the gastrointestinal tract.

Observation:

  • A 3-month-old infant presented with feeding refusal and "red-currant jelly" stools.
  • Abdominal ultrasound revealed a mass with characteristic intussusception features.
  • Laparotomy confirmed and resected the affected bowel segment.

Findings:

  • Histopathological examination of the resected segment revealed enteritis cystica profunda (ECP).
  • ECP was identified as the causative agent for the intussusception in this infant.
  • Literature review found only three similar pediatric cases in the past 30 years.

Implications:

  • Highlights ECP as a rare but significant cause of intussusception in infants.
  • Emphasizes the importance of considering rare etiologies in pediatric surgical emergencies.
  • Suggests a need for increased awareness of ECP in pediatric pathology and surgery.

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