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Anesthesia for the parturient with pseudoxanthoma elasticum.
M J Douglas1, V B Gunka, P von Dadelszen
1Department of Anaesthesia, University of British Columbia and British Columbia's Women's Hospital and Health Centre, Vancouver, BC, Canada. jdouglas@cw.bc.ca
International Journal of Obstetric Anesthesia
|January 29, 2005
Summary
Anesthetic management for patients with pseudoxanthoma elasticum (PXE) is feasible using regional techniques like epidural anesthesia during labor and cesarean delivery. These methods were safely employed in two cases, demonstrating no adverse effects from regional anesthesia in women with PXE.
Area of Science:
- Obstetrics and Anesthesiology
- Medical Genetics and Rare Diseases
Background:
- Pseudoxanthoma elasticum (PXE) is a rare genetic disorder affecting elastic tissues.
- Anesthetic management in pregnant patients with PXE requires careful consideration due to potential systemic complications.
Purpose of the Study:
- To describe the anesthetic management of two pregnant patients with pseudoxanthoma elasticum.
- To evaluate the safety and implications of regional anesthesia in this specific obstetric population.
Main Methods:
- Case report detailing anesthetic techniques used in two parturients with PXE.
- Review of anesthetic considerations for pseudoxanthoma elasticum in pregnancy.
Main Results:
- Successful labor analgesia with epidural catheter and forceps delivery in the first patient.
- Successful cesarean section under epidural anesthesia in the second patient, despite a complicated postoperative course.
- No adverse events directly attributed to regional anesthesia in either case.
Conclusions:
- Regional anesthesia, including epidural techniques, can be safely utilized in parturients with pseudoxanthoma elasticum.
- Careful preoperative assessment and planning are crucial for managing anesthesia in pregnant patients with PXE.