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Mitral valve morphology and morbidity/mortality in Shone's complex
Catherine M Ikemba1, Benjamin W Eidem, J Kennard Fraley
1University of Texas Southwestern, Children's Medical Center of Dallas, Division of Cardiology, Dallas, Texas, USA. catherine.ikemba@childrens.com
The American Journal of Cardiology
|February 8, 2005
Summary
Shone
Area of Science:
- Cardiology
- Pediatric Cardiology
- Echocardiography
Background:
- Shone's complex is a rare congenital heart defect.
- Early identification of risk factors is crucial for managing Shone's complex.
Purpose of the Study:
- To identify echocardiographic features predicting progressive mitral valve disease and mortality in Shone's complex.
- To evaluate the prognostic value of specific left-sided cardiac anomalies.
Main Methods:
- Retrospective analysis of echocardiographic data from 50 patients with Shone's complex.
- Assessment of mitral valve morphology, chordal structure, and associated flow dynamics.
- Correlation of echocardiographic findings with the need for intervention and mortality.
Main Results:
- Thickened mitral valve leaflets and shortened chordae were associated with poor outcomes.
- Left ventricular outflow tract obstruction (without coarctation) and aortic insufficiency also predicted a worse prognosis.
- Color Doppler findings of turbulence at or below the mitral valve were significant.
Conclusions:
- Specific echocardiographic features in early childhood can predict the need for intervention and mortality in Shone's complex.
- Early identification of these features allows for timely management and improved patient outcomes.