Odontogenic keratocyst in an infant

Odontogenic keratocysts occur as solitary lesions or in association with the basal cell naevus syndrome (BCNS), and have been documented in the age range 5 to 83 years. A rare case of an odontogenic keratocyst in a one-year-old girl is presented. Its characteristic tendency to recur, and its association with BCNS present important clinical implications.