Stenosis of the abdominal aorta caused by fibromuscular dysplasia

J Flores1, N Shiiya, K Matsuzaki

  • 1Departament of Cardiovascular Surgery, Hokkaido University School of Medicine, Hokkaido, Japan.

Insights

Fibromuscular dysplasia is a rare aortic disease. This case highlights infrarenal aortic stenosis caused by fibromuscular dysplasia in a middle-aged woman, emphasizing diagnosis and treatment options.

Area of Science:

  • Vascular Medicine
  • Cardiovascular Pathology

Background:

  • Fibromuscular dysplasia (FMD) is a rare, non-atherosclerotic vascular disease.
  • Aortic involvement, particularly infrarenal abdominal aorta stenosis, is exceptionally uncommon.

Observation:

  • A 49-year-old woman presented with intermittent claudication.
  • Angiographic findings revealed stenosis of the infrarenal abdominal aorta.

Findings:

  • Surgical aortic endarterectomy was performed.
  • Pathological examination confirmed fibromuscular dysplasia as the cause of stenosis.

Implications:

  • This case expands the understanding of rare aortic fibromuscular dysplasia presentations.
  • It underscores the importance of considering FMD in unexplained aortic stenosis.
  • Management strategies for this rare condition warrant further investigation.

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