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Desmoplastic fibroma of the skull in an infant
Soo-Han Yoon1, Se Hyek Kim, Yong Sam Shin
1Department of Neurosurgery, School of Medicine, Ajou University, Paldal-Gu, Wonchon-Dong, San#5, Suwon, South Korea.
Insights
This case report details a rare infantile desmoplastic fibroma (DF) of the skull, a benign bone tumor. Surgical excision successfully treated the tumor, with no recurrence observed in the first year post-operation.
Area of Science:
- Oncology
- Pediatric Surgery
- Pathology
Background:
- Desmoplastic fibroma (DF) is a rare, benign fibroblastic tumor.
- DF of the skull is exceptionally uncommon, particularly in infants.
Observation:
- A 1-year-old girl presented with a large osteolytic interosseous mass of the frontal skull.
- Imaging revealed the tumor extended to the frontal sinus and temporal base without intracranial invasion.
Findings:
- Surgical excision of the skull tumor was performed.
- Pathological examination confirmed the diagnosis of desmoplastic fibroma.
- The patient showed improved cranial asymmetry post-surgery.
Implications:
- This report describes the second known infantile case of skull desmoplastic fibroma.
- Successful surgical management highlights the importance of early diagnosis and intervention.
- Further research into pediatric skull DF is warranted given its rarity.
Case Report:
A 1-year-old girl presented with a 10-month history of progressive protuberance of the left frontal skull. Magnetic resonance imaging and computed tomography demonstrated a large osteolytic interosseous mass extending to the frontal sinus and temporal base without any intracranial invasion. A fronto-temporo-parietal craniectomy of the outer skull table and excision of an interosseous tumor resulted in local dural exposure in the temporal area that was covered by cranioplasty. Pathological examination identified desmoplastic fibroma (DF) of the skull. The patient's cranial asymmetry was improved without recurrence of the tumor up to the 12th month after excision.
Discussion:
In the literature, 11 cases of DF of the skull have been reported, two of which have involved children (one an infant). We report the second known infantile case of DF of the skull.
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