Papillary fibroelastoma of the mitral valve associated with rheumatic mitral valve stenosis

Iwao Taniguchi1, Keisuke Morimoto, Shigeto Miyasaka

  • 1Department of Thoracic Cardiovascular Surgery, Tottori Prefectural Central Hospital, Tottori, Japan.

The Japanese Journal of Thoracic and Cardiovascular Surgery : Official Publication of the Japanese Association for Thoracic Surgery = Nihon Kyobu Geka Gakkai Zasshi
|April 15, 2005
PubMed

Insights

Papillary fibroelastoma, a rare cardiac tumor, was diagnosed in a patient with mitral valve stenosis using echocardiography. Surgical removal and valve replacement were successful, with the patient remaining symptom-free post-operation.

Area of Science:

  • Cardiology
  • Cardiac Surgery
  • Pathology

Background:

  • Papillary fibroelastomas are rare cardiac tumors, often incidentally discovered.
  • Diagnosis in living patients is primarily achieved through echocardiography.
  • Co-occurrence with other cardiac conditions, like mitral valve stenosis, is uncommon.

Observation:

  • A 68-year-old woman presented with a diagnosed mitral valve tumor and severe rheumatic mitral valve stenosis.
  • The patient had a history of cerebral embolization treated with warfarin for 8 years.
  • Echocardiography confirmed a mitral valve mass and severe stenosis; electrocardiography showed chronic atrial fibrillation.

Findings:

  • Surgical excision of the papillary fibroelastoma and mitral valve replacement were performed.
  • Histological examination confirmed the diagnosis of papillary fibroelastoma.
  • The patient experienced an uneventful postoperative recovery and remained symptom-free at one year.

Implications:

  • This case highlights the successful diagnosis and surgical management of a rare papillary fibroelastoma coexisting with rheumatic mitral valve stenosis.
  • Echocardiography is crucial for diagnosing these rare cardiac tumors in symptomatic patients.
  • Multidisciplinary management involving cardiology, cardiac surgery, and pathology is essential for optimal outcomes in complex cardiac cases.

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