Related Experiment Videos
Perinephric angiomyolipoma: a unique development pattern surrounding the kidney.
Wataru Obara1, Kazunori Sato, Yukihisa Owari
1Department of Urology, Iwate Medical University School of Medicine, Morioka, Japan. watao@iwate-med.ac.jp
Summary
A rare case of extrarenal angiomyolipoma in the perinephric space presented with asymptomatic macrohematuria. This retroperitoneal mass, separate from the kidney, highlights the importance of considering rare diagnoses.
Area of Science:
- Urology
- Radiology
- Pathology
Background:
- Extrarenal angiomyolipomas (EAMLs) are rare benign tumors.
- Perinephric space EAMLs are exceptionally uncommon, posing diagnostic challenges.
Observation:
- A 31-year-old male presented with asymptomatic macrohematuria.
- Abdominal CT revealed a large perinephric mass distinct from the right kidney, encasing it.
Findings:
- The mass was diagnosed as an extrarenal angiomyolipoma of the perinephric fat.
- This highlights a rare presentation of angiomyolipoma outside the kidney.
Implications:
- EAMLs should be included in the differential diagnosis for retroperitoneal masses.
- Asymptomatic macrohematuria can be a presenting symptom of rare perinephric tumors.