Preserved systolic function with isolated left ventricular noncompaction in an elderly patient

Dursun Aras1, Omac Tufekcioglu, Serkan Topaloglu

  • 1Turkiye Yuksek Ihtisas Hospital, Department of Cardiology, Ankara, Turkey. sevgidursun06@yahoo.com

Insights

Isolated left ventricular noncompaction (IVNC) is a rare heart condition. This report details the oldest known case of IVNC in an elderly patient with preserved heart function.

Area of Science:

  • Cardiology
  • Genetics
  • Embryology

Background:

  • Isolated left ventricular noncompaction (IVNC) is a rare congenital cardiomyopathy.
  • It arises from abnormal endomyocardial embryogenesis.
  • Clinical features include heart dysfunction, embolism, and arrhythmias.

Observation:

  • A 78-year-old patient was diagnosed with IVNC.
  • The patient presented with preserved left ventricular systolic function.
  • This is the oldest reported case of IVNC with preserved LV function.

Findings:

  • IVNC can occur in elderly individuals.
  • Preserved left ventricular systolic function is possible in older IVNC patients.
  • The clinical characterization and natural course of IVNC in the elderly require further study.

Implications:

  • This case expands the known age range for IVNC diagnosis.
  • It highlights the importance of considering IVNC in elderly patients with heart conditions.
  • Further research is needed to understand IVNC's long-term effects in older populations.

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