Jove
Visualize
Contact Us
JoVE
x logofacebook logolinkedin logoyoutube logo
ABOUT JoVE
OverviewLeadershipBlogJoVE Help Center
AUTHORS
Publishing ProcessEditorial BoardScope & PoliciesPeer ReviewFAQSubmit
LIBRARIANS
TestimonialsSubscriptionsAccessResourcesLibrary Advisory BoardFAQ
RESEARCH
JoVE JournalMethods CollectionsJoVE Encyclopedia of ExperimentsArchive
EDUCATION
JoVE CoreJoVE BusinessJoVE Science EducationJoVE Lab ManualFaculty Resource CenterFaculty Site
Terms & Conditions of Use
Privacy Policy
Policies

Related Experiment Videos

[Aortic dissection associated with Turner's syndrome].

Y Ota1, M Tsunemoto, M Shimada

  • 1Department of Cardiovascular Surgery & Cardiology, National Children's Hospital.

Kyobu Geka. the Japanese Journal of Thoracic Surgery
|May 1, 1992
PubMed
Summary

Two Turner

Related Concept Videos

You might also read

Related Articles

Articles linked to this work by shared authors, journal, and citation graph.

Sort by
Same author

Turbulence Transition in Magnetically Confined Hydrogen and Deuterium Plasmas.

Physical review letters·2024
Same author

Characteristics of constrained turbulent transport in flux-driven toroidal plasmas.

Philosophical transactions. Series A, Mathematical, physical, and engineering sciences·2023
Same author

Measurement of Pa<sub>α</sub> line from pellet ablation cloud in Heliotron J.

The Review of scientific instruments·2022
Same author

Precise spectroscopy of <sup>167</sup>Er:Y<sub>2</sub>SiO<sub>5</sub> based on laser frequency stabilization using a fiber laser comb.

Optics express·2021
Same author

Persistence of Ion Temperature Gradient Turbulent Transport at Finite Normalized Pressure.

Physical review letters·2019
Same author

Application of portable near-infrared spectrometer to Heliotron J plasma diagnostics.

The Review of scientific instruments·2018

Area of Science:

  • Cardiovascular Surgery
  • Genetics
  • Pediatric Cardiology

Background:

  • Turner's syndrome is associated with cardiovascular abnormalities, including coarctation of the aorta.
  • Surgical repair of coarctation of the aorta in Turner's syndrome patients presents unique challenges.
  • Long-term complications following coarctation repair in this population require further investigation.

Observation:

  • Two cases of Turner's syndrome with prior coarctation repair experienced fatal complications.
  • Case 1: Developed aortic dissection and severe aortic regurgitation, leading to death post-valve replacement.
  • Case 2: Experienced aortic wall fragility, re-stenosis, aneurysm formation, and fatal rupture.

Findings:

  • Both patients died from complications attributed to Turner's stigmata and aortic pathology.
  • Cystic medionecrosis and bicuspid aortic valve were noted in Case 1.
  • Aortic aneurysm and rupture were critical events in Case 2.

Implications:

  • This highlights the critical need for vigilant long-term surveillance of cardiovascular health in Turner's syndrome patients post-coarctation repair.
  • Understanding the specific aortic tissue fragility in Turner's syndrome is crucial for surgical planning and risk assessment.
  • Further research into optimal management strategies for aortic abnormalities in Turner's syndrome is warranted.

Related Experiment Videos