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[A case of pure unroofed coronary sinus syndrome with persistent left superior vena cava]
Insights
A rare congenital heart defect, unroofed coronary sinus syndrome, was successfully treated in a 36-year-old woman. Surgical repair involved ligating the persistent left superior vena cava and closing an atrial septal defect, with no complications.
Area of Science:
- Cardiovascular Surgery
- Congenital Heart Defects
- Medical Case Reports
Background:
- Unroofed coronary sinus syndrome is a rare congenital anomaly.
- It involves the absence of the coronary sinus, coronary sinus atrial septal defect, and persistent left superior vena cava draining into the left atrium.
Observation:
- A 36-year-old woman presented with pure unroofed coronary sinus syndrome.
- The patient had an absent coronary sinus, coronary sinus ASD, and a persistent left superior vena cava draining into the left atrium.
Findings:
- Surgical intervention included ligation of the persistent left superior vena cava and closure of the atrial septal defect with a Dacron patch.
- Postoperative coronary arteriography confirmed the absence of the coronary sinus.
- No cerebral complications arose from increased intracranial pressure following the ligation.
Implications:
- This case highlights a successful surgical management strategy for pure unroofed coronary sinus syndrome.
- The findings suggest that prompt surgical correction can prevent serious postoperative complications.
- This case contributes to the understanding and treatment of rare cardiovascular anomalies.
Abstract:
A 36-year-old women with pure unroofed coronary sinus syndrome was reported. The anomalies of the cardiovascular system were absence of the coronary sinus, coronary sinus ASD and persistent left superior vena cava (PLSVC) draining into the left atrium. In this case, the PLSVC was ligated in the pericardium and the atrial septal defect was closed with a Dacron patch. There was no cerebral complication due to the increased intracranial pressure after ligation of the PLSVC. Postoperative coronary arteriography revealed absence of the coronary sinus in the venous phase.