A large left ventricular pseudoaneurysm in Behçet's disease: a case report

Seyed Mojtaba Marashi1, Payam Eghtesadi-Araghi, Mohammad Hussein Mandegar

  • 1Department of Cardiac Surgery, Dr. Shariati Hospital Complex, Tehran Univ. of Medical Sciences, Tehran 14197, Iran. marashi@doctor.com

BMC Surgery
|June 16, 2005
PubMed

Insights

Behçet

Area of Science:

  • Cardiovascular Medicine
  • Rheumatology
  • Vascular Surgery

Background:

  • Behçet's disease is a multisystem inflammatory disorder primarily affecting the vascular system.
  • While arterial pseudoaneurysms are common, cardiac involvement, particularly left ventricular pseudoaneurysms, is exceptionally rare.
  • This condition is more prevalent in Asian and Mediterranean populations.

Observation:

  • A case report details a 13-year-old male with a 4-year history of Behçet's disease.
  • The patient presented with symptoms including cough, chills, fever, and chest pain.
  • Diagnostic imaging, including echocardiography, MRI, CT, and coronary angiography, confirmed a large left ventricular pseudoaneurysm.

Findings:

  • Surgical intervention was performed for the left ventricular pseudoaneurysm.
  • The patient experienced no complications during a 24-month follow-up period post-surgery.
  • This case highlights the potential for rare cardiac manifestations in Behçet's disease.

Implications:

  • The nonspecific symptoms of cardiac pseudoaneurysms necessitate a high index of suspicion in Behçet's disease patients.
  • Early diagnosis and management are crucial due to the potentially fatal nature of cardiac pseudoaneurysms.
  • This case underscores the importance of considering cardiac complications in the long-term management of Behçet's disease.
Abstract

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