Congenital chylothorax in three siblings

Yao-Lung Chang1, Reyin Lien, Chin-Jung Wang

  • 1Department of Obstetrics and Gynecology, and Pediatric, Change Gung Memorial Hospital, Linkou Medical Center, Tao-Yuan Hsien, Taiwan. j12054@cgmh.org.tw

Congenital chylothorax is an uncommon condition, resulting from lymphatic accumulation in the fetal thorax; affected siblings are extremely rare. We report a woman who delivered 3 children with congenital chylothorax; each case was managed differently, including the use of ex utero intrapartum treatment (EXIT) with the third pregnancy.

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