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Cystic lymphangioma associated with enteric duplication as a cause of recurrent vomiting

L Quaglietta1, R Mastroianni, E Miele

  • 1Department of Paediatrics, University Federico II, Naples, Italy.

Digestive and Liver Disease : Official Journal of the Italian Society of Gastroenterology and the Italian Association for the Study of the Liver
|June 25, 2005
PubMed

Insights

A rare case report details a child initially diagnosed with Cyclical Vomiting Syndrome. The actual cause was an enteric duplication linked to cystic lymphangioma, a previously undescribed association.

Area of Science:

  • Pediatric Gastroenterology
  • Surgical Case Reports

Background:

  • Cyclical Vomiting Syndrome (CVS) is a functional gastrointestinal disorder characterized by recurrent episodes of intense nausea and vomiting.
  • Accurate diagnosis of CVS can be challenging, often requiring extensive investigation to rule out organic causes.

Observation:

  • A 6-year-old boy presented with a 4-year history of cyclical vomiting, initially managed as Cyclical Vomiting Syndrome.
  • Diagnostic workup revealed an enteric duplication cyst.
  • The enteric duplication was found to be associated with a cystic lymphangioma.

Findings:

  • The patient's cyclical vomiting was ultimately attributed to an enteric duplication cyst associated with cystic lymphangioma.
  • This specific combination of enteric duplication and cystic lymphangioma has not been previously documented in medical literature.

Implications:

  • Highlights the importance of considering rare organic etiologies even in cases presenting with classic features of functional disorders like CVS.
  • This case expands the known associations of enteric duplication cysts and cystic lymphangiomas.
  • Suggests further investigation may be warranted in refractory or atypical cases of cyclical vomiting.

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