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Cor triatriatum sinistrum: one institution's 28-year experience
A Gheissari1, J R Malm, F O Bowman
1Department of Surgery, Columbia Presbyterian Medical Center, New York, New York.
Pediatric Cardiology
|April 11, 1992
Summary
Cor triatriatum sinistrum, a rare congenital heart defect, often presents as congestive heart failure. Echocardiography is the preferred diagnostic tool, and surgical repair offers a low operative mortality for this potentially lethal condition.
Area of Science:
- Cardiology
- Pediatric Cardiology
- Congenital Heart Disease
Background:
- Cor triatriatum sinistrum is a rare congenital cardiac anomaly.
- It can lead to severe complications, including congestive heart failure.
- Accurate and timely diagnosis is crucial for effective management.
Purpose of the Study:
- To review the diagnosis and treatment of cor triatriatum sinistrum.
- To evaluate the effectiveness of echocardiography in diagnosing this condition.
- To assess the surgical outcomes for patients with cor triatriatum sinistrum.
Main Methods:
- Retrospective review of 12 patients with cor triatriatum sinistrum treated over 28 years.
- Analysis of diagnostic methods including cardiac catheterization, angiography, echocardiography, and autopsy.
- Evaluation of surgical approach and outcomes.
Main Results:
- Congestive heart failure was the most common presentation.
- Echocardiography demonstrated higher diagnostic accuracy compared to cardiac catheterization and angiography.
- Surgical treatment via a right atrial, transseptal approach with membrane excision was successful in most cases, with low operative mortality.
Conclusions:
- Cor triatriatum sinistrum is a rare but potentially lethal congenital heart anomaly.
- Echocardiography is the diagnostic modality of choice.
- Surgical intervention with a transseptal approach offers successful treatment with low mortality.