A neuro-Behçet's case complicated with intracranial hypertension successfully treated by a lumboperitoneal shunt

Hakan Erdem1, Ayhan Dinç, Salih Pay

  • 1Division of Rheumatology, Department of Medicine, Gülhane Military School of Medicine, Etlik/Ankara 06018, Turkey. herdem67@gata.edu.tr

Joint Bone Spine
|October 18, 2005
PubMed

Insights

Behçet

Area of Science:

  • Neurology
  • Rheumatology
  • Neurosurgery

Background:

  • Behçet's disease (BD) is a rare multisystem inflammatory disorder.
  • Dural sinus thrombosis (DST) is a serious neurological complication of BD.
  • Intracranial hypertension is a common manifestation of DST in BD.

Observation:

  • A 21-year-old male with Behçet's disease presented with dural sinus thrombosis.
  • Standard immunosuppressive therapy (acetazolamide, azathioprine, methylprednisolone) provided minimal relief for intracranial hypertension.
  • Frequent cerebrospinal fluid (CSF) drainage was required to manage symptoms.

Findings:

  • Lumboperitoneal shunting was performed due to persistent intracranial hypertension.
  • The shunt procedure led to rapid resolution of papilledema.
  • Gradual improvement in visual field deficits was observed post-shunting.

Implications:

  • Lumboperitoneal shunting is a viable therapeutic option for refractory intracranial hypertension in BD patients with DST.
  • This intervention can effectively manage neurological complications when immunosuppression fails.
  • Highlights the importance of considering surgical options for severe neurological manifestations of Behçet's disease.

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