Spontaneous rupture of choledochal cyst presenting in childhood

Demet Aydoğdu Kiresi1, Aydin Karabacakoğlu, Alaaddin Dilsiz

  • 1Department of Radiology, Selcuk University Meram Faculty of Medicine, Konya, Turkey.

Insights

Spontaneous rupture of choledochal cysts can be the first sign of the condition, presenting as bile-like fluid. This rare complication requires prompt diagnosis using imaging and intraoperative cholangiography.

Area of Science:

  • Pediatric Surgery
  • Gastroenterology
  • Medical Imaging

Background:

  • Choledochal cysts are congenital dilations of the bile ducts.
  • Spontaneous rupture is a rare but serious complication, often presenting without prior symptoms.
  • Early recognition is crucial for effective management.

Observation:

  • A 10-year-old girl presented with acute abdominal pain, vomiting, and elevated liver enzymes.
  • Imaging revealed a dilated common bile duct, a large cystic mass, and free intraperitoneal fluid.
  • No history of trauma was reported.

Findings:

  • The clinical presentation and imaging findings were consistent with spontaneous choledochal cyst rupture.
  • Elevated bilirubin and liver enzymes indicated biliary obstruction and liver damage.
  • Intraoperative cholangiography is recommended for definitive diagnosis.

Implications:

  • This case highlights the importance of considering spontaneous choledochal cyst rupture in pediatric patients with acute abdomen.
  • Prompt diagnosis and surgical intervention are essential to prevent complications.
  • Enhanced awareness among clinicians can improve patient outcomes.

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