Intracardiac leiomyomatosis: iliac vein to right-ventricular outflow tract

Edward S Bennett1, Navin S Arora, Martin Kay

  • 1Internal Medicine, Kyrenia Cardiac Center, Flushing, NY 11355, USA.

Insights

A rare case of intracardiac leiomyomatosis was diagnosed in a patient with hypertension and asthma. Surgical excision was successfully performed, offering a potential management strategy for this uncommon condition.

Area of Science:

  • Cardiology
  • Oncology
  • Pathology

Background:

  • A 58-year-old female with a history of hypertension and asthma underwent a routine physical examination.
  • A grade II/VI systolic ejection murmur and electrocardiogram abnormalities were identified, prompting further cardiac assessment.

Observation:

  • Diagnostic investigations included transthoracic echocardiography, transesophageal echocardiography, contrast-enhanced CT and MRI, and exploratory laparotomy.
  • These evaluations led to the diagnosis of intracardiac leiomyomatosis.

Findings:

  • The primary finding was intracardiac leiomyomatosis, a rare condition involving smooth muscle tumors within the heart.
  • Surgical excision was the chosen management strategy.

Implications:

  • This case highlights the importance of considering rare cardiac tumors in the differential diagnosis of cardiac murmurs and abnormalities.
  • Successful surgical management of intracardiac leiomyomatosis offers a potential therapeutic approach for affected individuals.
Abstract

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