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[Biventricular endomyocardiofibrosis associated with renal amyloidosis]
José Ramos Filho1, Carlos Alberto Fontes de Souza, Enzo Magrini
1Universidade São Francisco, Bragança Paulista, Rua Benjamin Arruda 126/1, CEP 12914-560 Bragança Paulista, SP. jramos-uti@uol.com.br
Insights
Endomyocardial fibrosis is a restrictive cardiomyopathy causing heart failure due to impaired ventricular filling. This case highlights endomyocardial fibrosis associated with renal amyloidosis.
Area of Science:
- Cardiology
- Pathology
Background:
- Endomyocardial fibrosis is a restrictive cardiomyopathy.
- It involves endocardial and myocardial fibrosis, leading to diastolic dysfunction.
Observation:
- The patient presented with clinical signs of heart failure.
- Biventricular endomyocardial fibrosis was diagnosed.
Findings:
- The patient had coexisting renal amyloidosis.
- This association is uncommon and requires careful etiological diagnosis.
Implications:
- This case underscores the importance of clinical examination for diagnosing the etiology of heart failure.
- Recognizing associations like endomyocardial fibrosis and renal amyloidosis is crucial for patient management.
Abstract:
Endomyocardiofibrosis is a restrictive cardiomyopathy characterized by fibrotic involvement of the endocardium and adjacent myocardium, and by diastolic dysfunction caused by changes in distensibility making ventricular filling inadequate while preserving the systolic function. Clinically, it appears as heart failure, but etiological symptomatic discernment, suspicion and a clinical examination would be necessary in order to make a correct etiological diagnosis. The case of a patient with biventricular endomyocardial fibrosis associated with renal amyloidosis is presented.
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