[Pancreatic involvement in Wegener's granulomatosis: a rare and difficult diagnosis]

Pancreatic involvement in the course of wegener's granulomatosis is rarely reported.

We report a case presenting as a pancreatic tumorlike lesion. We also discuss six further cases from the medical literature. Two of them had a tumorlike lesion, three had acute pancreatitis and the last had exocrine pancreatic insufficiency.

Treatment, association of corticoid and cyclophosphamide, is efficient if it is started quickly. So we think that this unusual manifestation of Wegener's granulomatosis should be recognized.