[Spontaneous rupture of a choledochal cyst in a 11-month-old girl]

L Harper1, F Lavrand, P Pietrera

  • 1Département de Chirurgie Pédiatrique, Hôpital Pellegrin-Enfants, CHU de Bordeaux, place Amélie-Raba-Léon, 33076 Bordeaux cedex, France. harper_luke@hotmail.com

Insights

Spontaneous rupture of a choledochal cyst is a rare but serious complication, particularly in young children. Early surgical intervention, including complete cyst excision, is crucial for managing this congenital biliary tract malformation.

Area of Science:

  • Pediatric Surgery
  • Gastroenterology
  • Congenital Malformations

Background:

  • Choledochal cysts are rare congenital biliary tract malformations.
  • While often asymptomatic, they can present with severe complications.
  • Spontaneous rupture is an uncommon but critical presentation, especially in infants.

Observation:

  • A case of an 11-month-old girl presenting with abdominal pain, fever, and vomiting is detailed.
  • Initial ultrasonography showed intraabdominal fluid, with no previously diagnosed choledochal cyst.
  • Laparotomy was performed for suspected choledochal cyst rupture.

Findings:

  • A choledochojejunostomy with Roux-en-Y was performed.
  • Spontaneous choledochal cyst rupture is most frequent in children under 4 years old.
  • The etiology is multifactorial, likely involving pancreatic reflux and cyst wall weakness.

Implications:

  • Choledochal cysts warrant early surgical management, ideally by 6 months of age.
  • Complete excision is essential due to the risk of malignant transformation.
  • Prompt diagnosis and surgical treatment are vital for favorable outcomes in pediatric patients.

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