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MR features of angiosarcoma in a patient with Maffucci's syndrome
Mototaka Miyake1, Ukihide Tateishi, Tetsuo Maeda
1Division of Diagnostic Radiology and Nuclear Medicine, National Cancer Center Hospital, Tokyo, Japan.
Abstract:
Maffucci's syndrome is a rare sporadic congenital disorder associated with multiple enchondromas and soft tissue hemangiomas. These bone and soft tissue tumors have the potential of malignant transformation to various histologic types: chondrosarcoma, osteosarcoma, fibrosarcoma, and angiosarcoma. We report a rare case of Maffucci's syndrome with soft tissue angiosarcoma of the leg to illustrate MRI findings with pathologic correlations.