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[A ten-year old boy with progressive neurologic outcome]
Inger Sandvig1, Bjørn Tennøe, Ann-Sofie Eriksson
1Barneklinikken, Rikshospitalet, 0027 Oslo. inger.sandvig@rikshospitalet.no
Summary
Rasmussen's encephalitis, a rare inflammatory brain condition, caused intractable epilepsy in a Norwegian child. Hemispherectomy surgery resulted in a seizure-free outcome, highlighting the importance of early diagnosis.
Area of Science:
- Neurology
- Pediatric Neurology
- Neuroinflammation
Background:
- Rasmussen's encephalitis is a rare, chronic inflammatory neurological disorder of unknown cause.
- It typically presents with intractable partial epilepsy and progressive hemiparesis.
Observation:
- A case study of a 10-year-old Norwegian boy with symptoms consistent with Rasmussen's encephalitis.
- Clinical presentation included intractable partial epilepsy and epilepsia partialis continua.
Findings:
- Cerebral MRI revealed unilateral right-sided cerebral atrophy and signal abnormalities in the grey and white matter.
- Surgical intervention with right-sided hemispherectomy led to complete seizure remission.
Implications:
- This case represents the first documented child with Rasmussen's encephalitis in Norway.
- The findings suggest Rasmussen's encephalitis may be underdiagnosed, emphasizing the need for early recognition and intervention.