Myoepithelial hamartoma causing small-bowel intussusception: a case report and literature review

Ryoichi Ikegami1, Yoshio Watanabe, Takahisa Tainaka

  • 1Department of Pediatric Surgery, Aichi Children's Health and Medical Center, 1-2 Osakada, Morioka-cho, 474-0031, Obu-city, Aichi, Japan. ryouiti_ikegami@mx.achmc.pref.aichi.jp

Insights

A rare tumor, myoepithelial hamartoma (MEH), caused intussusception in a 5-month-old infant. Surgical intervention was necessary after hydrostatic reduction failed, highlighting MEH as an unusual cause of pediatric intussusception.

Area of Science:

  • Pediatric Surgery
  • Gastrointestinal Pathology
  • Oncology

Background:

  • Intussusception is a common surgical emergency in infants and children.
  • Hydrostatic reduction is the primary treatment modality for ileo-ileal intussusception.
  • Tumors are an uncommon leading point for intussusception in the pediatric population.

Observation:

  • A 5-month-old female infant presented with ileo-ileal intussusception.
  • Initial management with hydrostatic reduction was unsuccessful.
  • Surgical exploration identified a 1.5 cm tumor as the leading point.

Findings:

  • Histopathological diagnosis confirmed the tumor as a myoepithelial hamartoma (MEH).
  • Myoepithelial hamartomas are rare neoplasms, particularly in pediatric small bowel intussusception.
  • This case highlights an atypical etiology for intussusception in a young child.

Implications:

  • Myoepithelial hamartomas should be considered in the differential diagnosis of pediatric intussusception, especially when standard reduction methods fail.
  • Early surgical intervention may be required for intussusception caused by intraluminal masses.
  • Further research into the occurrence and management of MEH in pediatric intussusception is warranted.

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