[Rasmussen syndrome. Clinical study]

Rasmussen's syndrome is a specific progressive disease affecting primarily one hemisphere, accompanied by intractable seizures and leading to severe neurologic and mental deficit. The authors present one child with frequent partial motor seizures and myoclonic seizures refractory to antiepileptic drug therapy who was diagnosed with epilepsia partialis continua. After a period of 15 months the patient develops a spastic right hemiparesis and mental degradation. Association of this signs of the clinical picture lead to the diagnostic of Rasmussen's syndrome who was confirmed by the presence of localized EEG abnormalities and imaging studies.