Heart transplantation after Fontan's procedure with bilateral cavopulmonary connections

T D T Tjan1, H H Scheld, C Schmid

  • 1Department of Thoracic and Cardiovascular Surgery, University Hospital Muenster, Muenster, Germany. st.d.t.tjan@ukmuenster.de

Insights

This case study details a heart transplant for a young female with complex congenital heart disease, utilizing a novel approach for superior vena cava reconstruction. The persistent left superior caval vein was successfully reanastomosed into the right atrium.

Area of Science:

  • Cardiology
  • Cardiovascular Surgery
  • Pediatric Cardiology

Background:

  • Complete Fontan procedure and bidirectional cavopulmonary connections present complex surgical challenges.
  • Congenital heart defects often require staged surgical palliation and may necessitate heart transplantation.

Observation:

  • A young female patient with three caval drainages post-Fontan procedure and bilateral bidirectional cavopulmonary connections was evaluated for orthotopic heart transplantation.
  • Hypoplastic innominate vein posed a reconstruction challenge during the transplant procedure.

Findings:

  • The persistent left superior caval vein was successfully reanastomosed into the recipient's right atrium via the coronary sinus.
  • This technique avoided reconstruction of the hypoplastic innominate vein, offering an alternative surgical strategy.

Implications:

  • This case demonstrates a feasible alternative surgical technique for managing complex venous anomalies during heart transplantation in Fontan patients.
  • The described approach may improve outcomes for select pediatric heart transplant recipients with challenging venous anatomy.

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