Related Experiment Video
Updated: Aug 8, 2026
06:26
Novel and Innovative Hybrid Technique for Type A Aortic Dissection
Published on: March 28, 2025
Coarctation of a right aortic arch
Thomas S Maxey1, Michael W Bradner, T Brett Reece
1Department of Surgery, College of Medicine, University of South Florida, Tampa, Florida, USA. tjmaxey@yahoo.com
Journal of Cardiac Surgery
|May 11, 2006
Summary
A rare congenital heart defect, right-sided aortic arch with coarctation, was found in a 4-year-old boy. Surgical repair via right thoracotomy is a safe treatment option for this complex anomaly.
Area of Science:
- Cardiology
- Congenital Heart Disease
- Pediatric Cardiac Surgery
Background:
- Right-sided aortic arch (RSAA) is a rare congenital anomaly.
- Coarctation of the aorta (CoA) is a common congenital defect, but rare with RSAA.
- Bicuspid aortic valve (BAV) is frequently associated with aortic arch anomalies.
Observation:
- A 4-year-old boy presented with a history of a stenotic bicuspid aortic valve.
- Further cardiac evaluation revealed a concomitant coarctation of a right-sided aortic arch.
- This combination represents an exceedingly rare congenital cardiac anomaly.
Findings:
- The study details a rare case of a right-sided aortic arch with concomitant coarctation in a pediatric patient.
- Thorough cardiac evaluation and detailed imaging are crucial due to the high frequency of associated anomalies.
- Surgical repair was successfully performed through a right thoracotomy.
Implications:
- This case highlights the importance of comprehensive cardiac assessment in patients with suspected or confirmed aortic arch anomalies.
- It underscores the feasibility and safety of surgical correction for this rare combined defect.
- Further research into the embryological origins and long-term outcomes of such rare anomalies is warranted.
Related Concept Videos
01:10The Arch of Aorta
The coronary arteries, originating from the ascending aorta, bifurcate from two sinuses located within the ascending aorta. Positioned just above the aortic semilunar valve, these sinuses house essential aortic baroreceptors and chemoreceptors, crucial for maintaining cardiac function. The left coronary artery and the right coronary artery branch off from the left posterior and anterior aortic sinuses, respectively.
Encircling the heart, the coronary arteries form a ring-like structure before...
Encircling the heart, the coronary arteries form a ring-like structure before...
01:30Aneurysm I: Introduction
An aortic aneurysm is a localized outpouching or dilation at a weak point in the artery wall. It may involve different parts of the aorta, such as the abdominal aorta, aortic arch, or thoracic aorta.Etiological factorsSeveral disorders are associated with aortic aneurysms.Congenital causes, such as primary connective tissue disorders like Marfan syndrome, impact the integrity and strength of connective tissues, notably affecting the aorta. Marfan syndrome is a genetic disorder that specifically...
01:14The Aorta
The aorta is the largest artery in the human body. It originates from the left ventricle of the heart and extends down to the abdomen, where it splits into two smaller arteries. Structurally, it can be divided into four main parts: the ascending aorta, the aortic arch, the thoracic aorta, and the abdominal aorta.
The average diameter of the aorta is approximately 2-3 cm, but the size can vary depending on the section of the aorta and the individual's age, sex, and body size. The aorta is...
The average diameter of the aorta is approximately 2-3 cm, but the size can vary depending on the section of the aorta and the individual's age, sex, and body size. The aorta is...
01:21Aneurysm II: Clinical Manifestations and Diagnostic Studies
Thoracic, aortic arch and abdominal aneurysms are significant vascular conditions that can present with various clinical manifestations and lead to serious complications. Understanding these manifestations and the appropriate diagnostic studies is essential for effective management and treatment.Thoracic Aortic AneurysmsThoracic aortic aneurysms often remain asymptomatic until they reach a size that impinges on adjacent structures. They typically cause deep, diffuse chest pain that radiates to...
01:15Thoracic Aorta
The thoracic section of the aorta begins at the T5 vertebra and extends to the T12 level at the diaphragm, initially progressing through the mediastinum to the left of the spinal column. Throughout its course in the thoracic segment, the thoracic aorta emits various offshoots known collectively as visceral and parietal branches. The branches that predominantly supply blood to visceral organs are termed visceral branches and include bronchial, pericardial, esophageal, and mediastinal arteries,...
01:22Aortic Regurgitation II: Clinical Features and Diagnostic Tests
Aortic valve regurgitation (AR) occurs when the aortic valve fails to close properly, allowing blood to flow backward from the aorta into the left ventricle. This backflow can result in two distinct clinical presentations: acute and chronic AR, each characterized by its own set of symptoms and physical findings.Acute Aortic RegurgitationAcute AR presents with a sudden onset of severe symptoms. Patients typically experience profound dyspnea (shortness of breath), chest pain, and signs of left...