Five chambered heart: a case report and brief review of literature

Ozer Badak1, Bahri Akdeniz, Ozhan Goldeli

  • 1Department of Cardiology, School of Medicine, Dokuz Eylul University, 35340, Inciralti, Izmir, Turkey. ozer.badak@deu.edu.tr

Insights

A rare congenital heart anomaly presented as chest pain and suspicious ischemia findings. Diagnostic imaging revealed a dilated left anterior descending coronary artery with an unusual fistulous connection to a septal chamber.

Area of Science:

  • Cardiology
  • Congenital Heart Disease
  • Medical Imaging

Background:

  • Myocardial ischemia can present with diverse etiologies.
  • Congenital coronary artery anomalies are uncommon but clinically significant.
  • Diagnostic challenges arise in identifying complex cardiac malformations.

Observation:

  • A patient presented with chest pain and initial findings suggestive of myocardial ischemia.
  • Electrocardiography and myocardial perfusion scintigraphy indicated potential coronary artery issues.
  • Further investigations included coronary angiography, echocardiography, and magnetic resonance imaging.

Findings:

  • A dilated left anterior descending coronary artery was identified.
  • This artery demonstrated a fistulous communication with a distinct chamber.
  • The anomalous chamber was located within the infero-apical interventricular septum.

Implications:

  • This case highlights a complex congenital anomaly requiring careful diagnostic evaluation.
  • Understanding such anomalies is crucial for accurate diagnosis and management.
  • The report discusses the clinical challenges posed by this rare cardiac malformation.

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