Partial hammock valve: surgical repair in adulthood

José I Aramendi1, Miguel A Rodríguez, Roberto Voces

  • 1Division of Cardiac Surgery, Hospital de Cruces, Barakaldo, Vizcaya, Spain. jiaramendi@hcru.osakidetza.net

Insights

A rare congenital heart defect, a forme fruste of hammock valve, affects only the posterior mitral leaflet. This previously unreported lesion causes severe mitral regurgitation in adults, requiring surgical repair.

Area of Science:

  • Cardiology
  • Congenital Heart Disease
  • Cardiac Surgery

Background:

  • Hammock valve is a rare congenital anomaly of the mitral valve.
  • This condition typically involves both mitral leaflets.
  • A forme fruste variant affecting only the posterior leaflet is described here.

Observation:

  • Three adult patients presented with severe mitral regurgitation.
  • Diagnosis of posterior leaflet fibrosis was suspected preoperatively.
  • Intraoperative findings revealed accessory papillary muscles attached to the posterior mitral leaflet.

Findings:

  • Accessory papillary muscles arranged in a palisade formation restricted posterior leaflet motion during systole.
  • This previously unreported congenital lesion manifests in adulthood.
  • Surgical repair involved dividing accessory papillary muscles, patch augmentation, and ring annuloplasty.

Implications:

  • This study identifies a novel congenital heart defect, a forme fruste of hammock valve.
  • Early recognition and surgical intervention are crucial for managing this condition.
  • Understanding this variant expands knowledge of mitral valve anomalies and their surgical management.