Recurrent nocturnal tongue biting in a child with hereditary chin trembling

Jatinder S Goraya1, Verinderjit Virdi, Veena Parmar

  • 1Section of Child Neurology, St Christopher's Hospital for Children, Philadelphia, PA 19134, USA.

Journal of Child Neurology
|November 10, 2006
PubMed

Insights

Hereditary chin trembling, a rare genetic disorder, caused tongue biting in a child during sleep. Clonazepam effectively treated the tongue biting, a symptom linked to parasomnia, but not the chin trembling itself.

Area of Science:

  • Neurology
  • Genetics
  • Sleep Medicine

Background:

  • Hereditary chin trembling is a rare autosomal dominant disorder.
  • It is characterized by involuntary mentalis muscle contractions.
  • This condition's presentation in India is reported for the first time.

Observation:

  • A 13-month-old boy experienced recurrent tongue biting episodes exclusively during sleep.
  • The patient was diagnosed with hereditary chin trembling.
  • Tongue biting was suspected to be a manifestation of parasomnia.

Findings:

  • Treatment with clonazepam successfully eliminated the tongue biting symptom.
  • Clonazepam did not impact the underlying chin trembling.
  • This suggests a specific link between parasomnia and tongue biting in this case.

Implications:

  • This case highlights a novel presentation of hereditary chin trembling.
  • It underscores the importance of considering parasomnia in sleep-related oral behaviors.
  • Pharmacological management with clonazepam may be beneficial for sleep-related tongue biting in similar cases.

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