Vestibular symptoms in children with enlarged vestibular aqueduct anomaly

J Fredrik Grimmer1, Gary Hedlund

  • 1Division of Otolaryngology, University of Utah, Primary Children's Medical Center, UT, USA. fred.grimmer@intermountainmail.org

Insights

Enlarged vestibular aqueduct (EVA) anomaly affects about half of patients with vestibular symptoms, with similar rates in pediatric and adult groups. Some patients may experience post-operative vertigo after cochlear implantation.

Area of Science:

  • Otolaryngology
  • Pediatric Audiology
  • Neuroscience

Background:

  • Enlarged vestibular aqueduct (EVA) is a common inner ear malformation.
  • Vestibular symptoms are frequently associated with EVA, impacting quality of life.
  • Understanding these symptoms in pediatric populations is crucial for management.

Purpose of the Study:

  • To characterize vestibular symptoms in pediatric patients diagnosed with enlarged vestibular aqueduct (EVA).
  • To compare vestibular symptom prevalence between pediatric and adult EVA patients.
  • To investigate post-operative vestibular symptoms following cochlear implantation in EVA patients.

Main Methods:

  • Retrospective chart review of patients with EVA anomaly.
  • Inclusion criteria: patients treated between 1995-2005 at specified medical centers.
  • Radiographic confirmation of EVA and comparison of symptom data between adult and pediatric cohorts.

Main Results:

  • Thirty-two patients (21 pediatric, 11 adult) were analyzed.
  • Vestibular symptom incidence was similar in pediatric (48.0%) and adult (45.5%) groups.
  • Four of 14 patients (28.6%) who underwent cochlear implantation reported post-operative vertigo.

Conclusions:

  • Approximately 50% of patients with EVA experience vestibular symptoms.
  • Pediatric and adult EVA patients exhibit comparable frequencies of vertigo and vestibular issues.
  • Cochlear implantation in EVA patients can lead to post-operative vestibular symptoms.
Abstract

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