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Related Concept Videos

Hearing01:31

Hearing

When we hear a sound, our nervous system is detecting sound waves—pressure waves of mechanical energy traveling through a medium. The frequency of the wave is perceived as pitch, while the amplitude is perceived as loudness.
The Auditory Ossicles01:11

The Auditory Ossicles

The auditory ossicles of the middle ear transmit sounds from the air as vibrations to the fluid-filled cochlea. The auditory ossicles consist of two malleus (hammer) bones, two incus (anvil) bones, and two stapes (stirrups), one on each side. These bones develop during the fetal stage and are the ones to ossify first. They are fully mature at birth and do not grow afterward.
The aptly named stapes look very much like a stirrup. The three ossicles are unique to mammals, and each plays a role in...
Auditory Pathway01:15

Auditory Pathway

Auditory pathways constitute the complex neural circuits responsible for transmitting and interpreting auditory information from the peripheral auditory system to the brain. Sound waves are initially captured by the outer ear, funneled through the ear canal, and reach the tympanic membrane (eardrum). These vibrations are transmitted via the middle ear's ossicles to the inner ear's cochlea.
When viewed cross-sectionally, the cochlea reveals the scala vestibuli and scala tympani flanking the...
Auditory Perception01:17

Auditory Perception

The auditory system is essential for sound perception, utilizing various critical structures. When sound waves enter the outer ear, they travel through the ear canal and cause the eardrum to vibrate. These vibrations are then transmitted to the middle ear, where three tiny bones – the malleus, incus, and stapes – amplify the sound. This amplification is crucial, as it ensures that the sound vibrations are strong enough to be conveyed to the inner ear. These vibrations then reach the cochlea, a...
Anatomy of the Ear01:16

Anatomy of the Ear

Auditory sensation, commonly called hearing, involves the transformation of sonic waves into neural impulses facilitated by the structures of the auditory organ. The prominent, flesh-like structure on the side of the head, called the auricle, directs sound waves towards the auditory canal. The auricle is often mislabeled as the pinna, a term more aligned with mobile structures like a feline's external ear. The auditory canal penetrates the cranium via the external auditory meatus of the...

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Related Experiment Video

Updated: Jul 18, 2026

Quantitative Assessment of Cortical Auditory-tactile Processing in Children with Disabilities
09:38

Quantitative Assessment of Cortical Auditory-tactile Processing in Children with Disabilities

Published on: January 29, 2014

[Auditory function in children with Brachmann-de Lange syndrom].

Jacek Kozłowski1, Jolanta Wierzba, Waldemar Narozny

  • 1Katedra i Klinika Chorób Uszu, Nosa, Gardła i Krtani AM w Gdańsku.

Otolaryngologia Polska = the Polish Otolaryngology
|December 13, 2006
PubMed
Summary

Half of children with Brachmann-de Lange syndrome experience hearing loss. Early auditory evoked potential testing is crucial for timely intervention and preventing developmental delays.

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Behavioral Assessment of Hearing in 2 to 4 Year-old Children: A Two-interval, Observer-based Procedure Using Conditioned Play-based Responses
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Behavioral Assessment of Hearing in 2 to 4 Year-old Children: A Two-interval, Observer-based Procedure Using Conditioned Play-based Responses

Published on: January 23, 2017

Related Experiment Videos

Last Updated: Jul 18, 2026

Quantitative Assessment of Cortical Auditory-tactile Processing in Children with Disabilities
09:38

Quantitative Assessment of Cortical Auditory-tactile Processing in Children with Disabilities

Published on: January 29, 2014

Behavioral Assessment of Hearing in 2 to 4 Year-old Children: A Two-interval, Observer-based Procedure Using Conditioned Play-based Responses
14:05

Behavioral Assessment of Hearing in 2 to 4 Year-old Children: A Two-interval, Observer-based Procedure Using Conditioned Play-based Responses

Published on: January 23, 2017

Area of Science:

  • Genetics
  • Audiology
  • Pediatrics

Context:

  • Brachmann-de Lange syndrome is a rare genetic disorder.
  • Auditory function is often affected in children with this syndrome.
  • Early detection of hearing loss is critical for development.

Purpose:

  • To evaluate auditory function in children with Brachmann-de Lange syndrome.
  • To assess the prevalence of hearing loss in this population.
  • To determine the necessity of auditory screening.

Summary:

  • This study examined 18 children with Brachmann-de Lange syndrome.
  • Brainstem auditory evoked potential and tympanometry were performed.
  • Hearing loss was identified in 50% of the children.

Impact:

  • Early auditory evoked potential screening is recommended for all children with Brachmann-de Lange syndrome.
  • Timely intervention for hearing loss can prevent social isolation and developmental issues.
  • Proper management of hearing impairment supports communication and cognitive progress.