[Hand involvement in Thevenard's disease: a new "phlegmonous" form. An exceptional case report]

Thévenard's disease is a rare familial ulcero-mutilating acropathology involving the peripheral nervous system. It typically begins on the feet and only rarely spreads to the hands late in the course of the disease. It first causes cutaneous ulcerations and then secondary osseous deformations and osteoarticular destruction, due to a distal loss of temperature sensation. We report the case of an 87 year old patient who suffered from a particular clinical form, undescribed as yet in the literature and characterized by local and general superinfections predominately on the hands. We term this the "cellulitic" presentation or form of Thévenard's disease.