Dental trauma after cardiac syncope in a patient with long QT syndrome

Dental trauma secondary to a syncopal episode occurs rarely in the pediatric population. Although the majority of these events occurs in patients with a benign medical history, a subset of these cases occur in patients with a genetic predisposition to cardiac arrhythmia. Long QT syndrome, characterized by prolonged cardiac ventricular repolarization, represents one genetic condition in which patients sustain events of seizure, syncope, and sudden cardiac death in response to precipitating physical, mental, or emotional stressors. In this case report, extensive dental injuries occurred after an episode of cardiac syncope in a patient with a dual presentation of long QT syndrome and Pierre Robin sequence. The purpose of this paper was to highlight the potentially malignant course of symptomatic long QT syndrome and emphasize the importance of warning sign recognition and multidisciplinary medical management of pediatric patients with this condition.