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Updated: Jul 16, 2026
04:44
Imaging Features of Systemic Sclerosis-Associated Interstitial Lung Disease
Published on: June 16, 2020
Systemic sclerosis
R S Ahathya1, D Deepalakshmi, Pamela Emmadi
1Department of Periodontics, Meenakshi Ammal Dental College and Hospital, Alapakkam Main Road, Maduravoyal, Chennai - 600 095, India. dr_ahathya@yahoo.co.in
Summary
Systemic sclerosis, a rare connective tissue disease, is typically diagnosed clinically. This case report details a 26-year-old female with classic scleroderma features, highlighting its rarity and varied presentation.
Area of Science:
- Rheumatology
- Internal Medicine
- Connective Tissue Diseases
Background:
- Systemic sclerosis (scleroderma) is a rare, generalized connective tissue disorder.
- Diagnosis is primarily clinical, relying on signs and symptoms.
Observation:
- Presents a case report of a 26-year-old female patient.
- The patient exhibited classical features of systemic sclerosis.
Findings:
- The case is notable for the rarity of the condition.
- Highlights the variable expressivity of systemic sclerosis.
- Literature review of this uncommon condition is included.
Implications:
- Contributes to understanding the clinical presentation of systemic sclerosis.
- Emphasizes the importance of clinical diagnosis in rare diseases.
- Provides insights into the variable nature of scleroderma.
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