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Bowel obstruction due to diaphragmatic hernia in an elder child after pediatric liver transplantation
Hideaki Okajima1, Shintaro Hayashida, Hironori Iwasaki
1Department of Transplantation/Pediatric Surgery, Postgraduate School of Medical Science, Kumamoto University, Kumamoto, Japan. hokajima@fc.kuh.kumamoto-u.ac.jp
Insights
A pediatric liver transplant recipient developed a diaphragmatic hernia, a rare complication after using a left lateral segment graft. Prompt surgical repair led to a full recovery, highlighting the need for vigilance in post-transplant care.
Area of Science:
- Hepatology
- Pediatric Surgery
- Transplantation Immunology
Background:
- Wilson's disease is a genetic disorder causing copper accumulation, often leading to end-stage liver cirrhosis.
- Living donor liver transplantation (LDLT) is a viable option for pediatric patients with end-stage liver disease.
- Left lateral segment grafts are commonly used in pediatric LDLT due to donor size limitations.
Observation:
- A 10-year-old boy with Wilson's disease underwent LDLT using his father's left lateral segment graft.
- Postoperatively, the patient experienced two episodes of bowel obstruction.
- The second episode presented with respiratory distress, revealing diaphragmatic hernia with intestinal herniation into the thoracic cavity.
Findings:
- Diaphragmatic hernia is a rare but significant complication following LDLT, particularly with left lobe or left lateral segment grafts.
- Surgical repair of the diaphragmatic hernia was successfully performed.
- The patient recovered well after the diaphragmatic hernia repair.
Implications:
- This case underscores the importance of recognizing diaphragmatic hernia as a potential complication after pediatric LDLT with specific graft types.
- Awareness and prompt diagnosis are crucial for effective management and improved patient outcomes.
- Further research may explore preventative strategies or optimized monitoring protocols for diaphragmatic hernia post-LDLT.
Abstract:
A 10-yr-old boy with end-stage liver cirrhosis due to Wilson's disease received a living donor liver transplantation (LDLT) at our institution. The donor was his father and the graft was a left lateral segment. The liver transplantation procedure and the postoperative course were uneventful. Two months after the procedure, he developed a first episode of bowel obstruction that was treated with conservative therapy. During a second episode of bowel obstruction, he also presented respiratory distress. A plain chest X-ray revealed the presence of small intestine loops in the right thoracic cavity and bowel obstruction due to diaphragmatic hernia was diagnosed. Repair of the diaphragmatic hernia was performed and the patient has been doing well after the surgery. Diaphragmatic hernia after LDLT is rare but should be recognized as a possible complication when a left lobe or a left lateral segment graft is used.
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