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Published on: April 26, 2019

Life after definitive treatment for children with Hirschsprung's disease

H Athanasakos1, J Starling, F Ross

  • 1Department of Academic Surgery, Children's Hospital at Westmead.

International Journal of Surgery (London, England)
|April 28, 2007
PubMed

Insights

Long-term outcomes for Hirschsprung

Area of Science:

  • Pediatric Surgery
  • Gastroenterology
  • Psychology

Background:

  • Hirschsprung's Disease (HD) is a congenital condition affecting the large intestine.
  • Surgical correction is the standard treatment for HD.
  • Long-term functional and psychosocial outcomes require further investigation.

Purpose of the Study:

  • To evaluate long-term outcomes post-surgical correction for Hirschsprung's Disease.
  • To assess the psychosocial impact of HD on affected children and their families.

Main Methods:

  • A cohort of 72 children and young adults (1-24 years) with HD and their families were studied.
  • A condition-specific questionnaire assessed functional and psychosocial outcomes.
  • Parental perceptions of long-term condition impact were gathered.

Main Results:

  • Faecal soiling was the most common functional issue (76.3%) post-surgery.
  • Younger children (<12 years) experienced more distress and family difficulties (73.6%) compared to older individuals (>12 years).
  • Despite challenges, young adults with HD (>12 years) reported confidence (62.5%) and hope for the future; parental marital relationships were impacted in 12.5% of cases.

Conclusions:

  • Functional issues and psychosocial distress in Hirschsprung's Disease improve with age and support.
  • Addressing condition-specific challenges, like faecal soiling, is crucial for better psychosocial adjustment.
Abstract

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