Modified oral rehydration therapy in a case with cystic fibrosis

S Songül Yalçin1, Tülay Akça, Ozge Genç

  • 1Department of Pediatrics, Hacettepe University, Faculty of Medicine, Ankara, Turkey.

Insights

Infants with cystic fibrosis may experience dehydration. Modified oral rehydration solutions effectively managed a case of pseudo-Bartter syndrome when intravenous access was impossible, stabilizing serum sodium levels.

Area of Science:

  • Pediatrics
  • Gastroenterology
  • Endocrinology

Background:

  • Cystic fibrosis (CF) infants are prone to hyponatremic, hypochloremic dehydration with metabolic alkalosis.
  • Management of this condition can be challenging, particularly when intravenous access is not feasible.

Observation:

  • A nine-month-old infant with CF presented with pseudo-Bartter syndrome.
  • The infant could not receive intravenous rehydration due to inaccessible routes.

Findings:

  • Modified oral rehydration solutions were administered to the infant.
  • Treatment led to a decreased purging rate and improved, stable serum sodium levels.

Implications:

  • Modified oral rehydration solutions offer a viable alternative for managing dehydration in CF infants when intravenous access is impossible.
  • These solutions can help stabilize electrolyte imbalances and improve clinical outcomes in challenging pediatric cases.

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