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Congenital hypothyroidism and cystic fibrosis
C Depasse1, J P Chanoine, G Casimir
1Department of Paediatrics, Hôpital Universitaire des Enfants Reine Fabiola, Université Libre de Bruxelles, Belgium.
Acta Paediatrica Scandinavica
|October 1, 1991
Abstract:
We report a case of dysgenetic congenital hypothyroidism associated with cystic fibrosis. Impaired exocrine pancreatic secretion and/or transit abnormalities secondary to the treatment of meconium ileus resulted in decreased absorption of L-thyroxine and difficulties in management of hypothyroidism.