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Steroid-responsive chorea in moyamoya disease
S G Pavlakis1, S Schneider, K Black
1Department of Pediatrics, North Shore University Hospital, New York City, New York.
Summary
Steroid therapy may help reduce disabling chorea symptoms in patients with moyamoya disease. However, perioperative steroids can impact neurosurgical outcomes, making it difficult to assess surgical effectiveness.
Area of Science:
- Neurology
- Pediatrics
- Neurosurgery
Background:
- Moyamoya disease is a rare cerebrovascular disorder characterized by progressive stenosis of the internal carotid arteries.
- Chorea is a hyperkinetic movement disorder that can be a disabling symptom in moyamoya disease, particularly in pediatric patients.
- The management of moyamoya-associated chorea remains challenging, with limited evidence on effective therapeutic interventions.