Related Experiment Video
Updated: Jul 13, 2026

Surgical Treatment of an Endolymphatic Sac Tumor
Published on: May 26, 2023
Sturge-Weber syndrome accompanied with multiple congenital intracranial lesions
R Ergün1, A I Okten, Y Gezercan
1Department of Neurosurgery, Abant Izzet Baysal University, Bolu, Turkey. ruchanergun@hotmail.com
Abstract:
Sturge-Weber syndrome is one of the neurocutaneous syndromes. It is a rare, nonfamiliar disease that is characterized by facial port-wine stain, leptomeningeal angiomatosis, choroidal angioma, buphthalmos, intracranial calcification, cerebral atrophy, mental retardation, glaucoma, seizures and hemiparesis. CT and MR are complementary in the evaluation of this disease. Epilepsy is an essential feature of Sturge-Weber syndrome and it has a major significance for prognosis and treatment. We report a 2-year-old boy with Sturge-Weber syndrome who had in addition an intracranial lipoma, a temporal arachnoid cyst and a porencephalic cyst. This combination of intracranial lesions with Sturge-Weber syndrome has not been previously reported.
Related Concept Videos
Increased Intracranial Pressure ll: Pathophysiology
Aneurysm II: Clinical Manifestations and Diagnostic Studies
Cerebral Edema ll: Pathophysiology
Increased Intracranial Pressure l: Introduction
Hemorrhagic Stroke ll: Pathophysiology
Pleiotropy
