Saccular aneurysm of congenital coronary arteriovenous fistula

K M Krishnamoorthy1, Sekhar Rao

  • 1Department of Cardiology, Sri Sathya Sai Institute of Higher Medical Sciences, Puttaparthi-515 134, India. saikm@sctimst.ker.nic.in

Insights

A rare congenital coronary arteriovenous fistula with an aneurysm was successfully treated by surgical closure of the drainage site and fistula ligation. This case highlights effective management of a complex cardiac anomaly.

Area of Science:

  • Cardiology
  • Cardiovascular Surgery
  • Medical Imaging

Background:

  • Congenital coronary arteriovenous fistulas are rare vascular anomalies.
  • Aneurysmal dilation within these fistulas presents unique diagnostic and therapeutic challenges.

Purpose of the Study:

  • To report a rare case of a congenital coronary arteriovenous fistula with an aneurysm.
  • To describe the diagnostic approach and successful surgical management of this condition.

Main Methods:

  • Echocardiography and selective angiography were used for diagnosis.
  • Surgical intervention involved cardiopulmonary bypass, direct closure of the fistula drainage into the right atrium, and ligation at the fistula origin.

Main Results:

  • Echocardiography revealed a dilated left circumflex artery with an aneurysm.
  • Selective angiography confirmed the aneurysm and its drainage into the posterior right atrial wall.
  • Successful surgical repair was achieved with direct closure and ligation.

Conclusions:

  • Congenital coronary arteriovenous fistulas with aneurysms, though rare, require precise diagnosis and tailored surgical intervention.
  • Direct surgical closure and ligation offer an effective treatment modality for such complex cases.

Related Concept Videos

Aneurysm I: Introduction01:30

Aneurysm I: Introduction

An aortic aneurysm is a localized outpouching or dilation at a weak point in the artery wall. It may involve different parts of the aorta, such as the abdominal aorta, aortic arch, or thoracic aorta.Etiological factorsSeveral disorders are associated with aortic aneurysms.Congenital causes, such as primary connective tissue disorders like Marfan syndrome, impact the integrity and strength of connective tissues, notably affecting the aorta. Marfan syndrome is a genetic disorder that specifically...
Coronary Circulation01:21

Coronary Circulation

The heart, an organ critical to survival, gets nourishment not from the blood it pumps but from a separate circulation system known as coronary circulation. This is the shortest circulation in the body and is responsible for supplying the heart with the nutrients it needs to function effectively.
Coronary circulation begins at the base of the aorta, where two main arteries arise—the left and right coronary arteries. These arteries encircle the heart in the coronary sulcus and supply the...
Aneurysm III: Interprofessional Care01:26

Aneurysm III: Interprofessional Care

Aneurysm management involves either conservative medical therapy or surgical intervention, depending on the size and symptoms of the aneurysm. Conservative management is generally reserved for smaller, asymptomatic aneurysms, while larger or symptomatic aneurysms often necessitate surgical repair.Conservative Medical TherapyFor small, asymptomatic aneurysms, particularly abdominal aortic aneurysms (AAA) less than 5.5 centimeters in diameter, conservative medical therapy is recommended. This...
Fetal Circulation01:14

Fetal Circulation

Fetal circulation is a unique system that facilitates the exchange of gases, nutrients, and waste products between the developing fetus and the mother. This intricate process takes place through a special organ called the placenta.
Two umbilical arteries transport blood from the fetus to the placenta. At the placenta, the blood absorbs oxygen and nutrients while simultaneously eliminating waste products. This oxygen-enriched and nutrient-rich blood then returns to the fetus through one...
Chambers of the Heart01:16

Chambers of the Heart

The human heart is a complex organ made up of four chambers: the right and left atria and the right and left ventricles. These internal chambers are separated by partitions known as the interatrial and interventricular septa. The exterior of the heart features a groove known as the coronary sulcus that demarcates the atria from the ventricles, while the anterior and posterior interventricular sulci distinguish between the two ventricles.
Deoxygenated blood from the body is received in the right...
Development of the Heart01:27

Development of the Heart

The development of the human heart, a crucial organ, commences from the mesoderm on the 18th or 19th day after fertilization. This process initiates in the cardiogenic area, a group of mesodermal cells at the embryo's head end, which evolves into elongated strands known as cardiogenic cords. These cords undergo a transformation to form hollow-centered endocardial tubes.
As the embryo undergoes lateral folding, these paired tubes approach each other, merging into a single primitive heart tube by...