Primary rhabdomyosarcoma of the right atrium

Rhabdomyosarcoma is the rare malignant tumor of the heart. A case of a large malignant rhabdomyosarcoma in a 37 year old woman is presented. The tumor arose from the anterior wall of the right atrium and was treated by surgical resection with replacement of the tricuspid valve with bioprosthesis. The patient passed two courses of adjuvant chemotherapy. Six months later transthoracic echocardiography revealed absence of any tissue masses in right atrium, superior vena cava and normal function of the bioprosthesis.