Right coronary artery to superior vena cava fistula presenting with 'steal' phenomenon

Sebastian Pagni1, Erle H Austin, Joseph S Abraham

  • 1Division of Thoracic and Cardiovascular Surgery, Department of Surgery, University of Louisville, Louisville, KY, USA. jwalsh@ucsamd.com

Insights

A rare coronary arteriovenous fistula connecting the right coronary artery to the superior vena cava caused myocardial ischemia. This case highlights a unique presentation of coronary artery anomalies.

Area of Science:

  • Cardiology
  • Vascular Surgery
  • Anatomical Abnormalities

Background:

  • Coronary arteriovenous fistulas (CAVF) are uncommon congenital or acquired abnormalities.
  • Right coronary artery (RCA) to superior vena cava (SVC) fistulas are particularly rare variations.

Purpose of the Study:

  • To report a unique case of a right coronary artery to superior vena cava fistula.
  • To describe the clinical presentation of myocardial ischemia secondary to this fistula.

Main Methods:

  • Case report detailing clinical presentation, diagnostic workup, and management.
  • Review of relevant literature on coronary arteriovenous fistulas.

Main Results:

  • The patient presented with symptoms of myocardial ischemia.
  • Diagnostic imaging confirmed a fistula between the RCA and SVC.

Conclusions:

  • Coronary arteriovenous fistulas, though rare, can lead to significant cardiac events like myocardial ischemia.
  • Accurate diagnosis and understanding of these anomalous connections are crucial for patient management.

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