Right coronary artery to superior vena cava fistula presenting with 'steal' phenomenon
Sebastian Pagni1, Erle H Austin, Joseph S Abraham
1Division of Thoracic and Cardiovascular Surgery, Department of Surgery, University of Louisville, Louisville, KY, USA. jwalsh@ucsamd.com
Insights
A rare coronary arteriovenous fistula connecting the right coronary artery to the superior vena cava caused myocardial ischemia. This case highlights a unique presentation of coronary artery anomalies.
Area of Science:
- Cardiology
- Vascular Surgery
- Anatomical Abnormalities
Background:
- Coronary arteriovenous fistulas (CAVF) are uncommon congenital or acquired abnormalities.
- Right coronary artery (RCA) to superior vena cava (SVC) fistulas are particularly rare variations.
Purpose of the Study:
- To report a unique case of a right coronary artery to superior vena cava fistula.
- To describe the clinical presentation of myocardial ischemia secondary to this fistula.
Main Methods:
- Case report detailing clinical presentation, diagnostic workup, and management.
- Review of relevant literature on coronary arteriovenous fistulas.
Main Results:
- The patient presented with symptoms of myocardial ischemia.
- Diagnostic imaging confirmed a fistula between the RCA and SVC.
Conclusions:
- Coronary arteriovenous fistulas, though rare, can lead to significant cardiac events like myocardial ischemia.
- Accurate diagnosis and understanding of these anomalous connections are crucial for patient management.
Abstract:
A coronary arteriovenous fistula is a rare occurrence. We report a case of a right coronary artery to superior vena cava fistula presenting with myocardial ischemia.
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