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Published on: October 20, 2017
Chiari malformation type III treated with primary closure
Ramandeep Singh Jaggi1, Ishwar Chandra Premsagar
1Department of Neurosurgery, Dr. R.M.L. Hospital, New Delhi, India.
Pediatric Neurosurgery
|September 6, 2007
Summary
This case report details a rare Type III Chiari malformation in an infant, presenting as a neck swelling. Surgical intervention successfully addressed the meningoencephalocele and cerebellar herniation.
Area of Science:
- Neurology
- Pediatric Neurosurgery
- Medical Genetics
Background:
- Chiari malformations encompass diverse hindbrain abnormalities.
- Type III Chiari malformation is exceptionally rare, with limited documented cases.
Observation:
- A 1-month-old female infant presented with a congenital neck swelling.
- MRI confirmed Type III Chiari malformation with high cervical meningoencephalocele and cerebellar herniation through a C2 defect.
Findings:
- Surgical excision of the meningoencephalocele and associated gliotic cerebellar tissue was performed.
- Posterior fossa decompression and augmentation duraplasty were key surgical components.
Implications:
- This case highlights the surgical management of a rare pediatric Chiari malformation.
- Successful surgical outcomes are possible with prompt diagnosis and intervention.
