Devic's neuromyelitis optica in an infant case

Deniz Yuksel1, Nesrin Senbil, Deniz Yilmaz

  • 1Department of Pediatric Neurology, Dr Sami Ulus Children's Health and Diseases Training and Research Hospital, Ankara, Turkey. drdeniz_yuksel@yahoo.com.tr

Journal of Child Neurology
|September 25, 2007
PubMed

Insights

Devic's neuromyelitis optica, a severe neurological syndrome, can affect children. This case report details a 23-month-old boy with Devic's neuromyelitis optica who experienced a poor treatment response and significant long-term effects.

Area of Science:

  • Neurology
  • Pediatric Neurology
  • Neuroimmunology

Background:

  • Devic's neuromyelitis optica (NMO) was historically defined as an acute, severe, monophasic syndrome involving myelitis and optic neuritis.
  • While typically presenting in adults around age 40, NMO has been observed in pediatric populations.
  • The prognosis for NMO was historically poor with limited treatment options.

Observation:

  • This report details a case of Devic's neuromyelitis optica in a 23-month-old boy.
  • The child presented with acute myelitis and optic neuritis, consistent with NMO diagnosis.
  • The pediatric patient exhibited a poor response to therapeutic interventions.

Findings:

  • The pediatric patient diagnosed with Devic's neuromyelitis optica developed severe sequelae.
  • This case highlights the potential for severe outcomes in young children with NMO.
  • The findings underscore the challenges in managing NMO in the pediatric population.

Implications:

  • This case emphasizes the need for early recognition and aggressive management of Devic's neuromyelitis optica in children.
  • Further research is warranted to explore effective therapeutic strategies for pediatric NMO.
  • Understanding NMO in children is crucial for improving long-term prognoses and reducing disability.

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