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Updated: Jul 11, 2026

Modified Posterior Vertebral Column Resection for Patients with Thoracolumbar Kyphotic Deformity
Published on: September 16, 2022
Unusual association of congenital kyphosis and conus lipoma presenting as a double spinal cord tether
Carlos A Aguiar1, Sergio Mendoza-Lattes, Peter Cobb
1Hospital Pequeno Principe, Ortopedia Pediatrica, R. Desembargador Motta, 1070 Curitiba, Parana, Brasil.
Insights
This case study details a child with congenital kyphosis and tethered cord syndrome. Surgical intervention successfully reversed paraparesis, highlighting effective treatment for spinal cord compression.
Area of Science:
- Pediatric Neurosurgery
- Spinal Deformity Correction
Background:
- Congenital kyphosis and tethered cord syndrome can lead to progressive neurological deficits in children.
- Early diagnosis and intervention are crucial for managing spinal cord compression.
Observation:
- A four-year-old child presented with cervicothoracic deformity and paraparesis.
- Imaging revealed severe congenital kyphosis, hypoplastic T3 vertebra, tethered filum terminale, and conus lipoma causing spinal cord compression.
Findings:
- Surgical release of the tethered cord and conus lipoma removal were performed.
- Subsequent kyphectomy and upper thoracic fusion addressed the spinal deformity.
- Complete reversal of paraparesis was achieved post-operatively.
Implications:
- This case demonstrates the successful management of complex spinal conditions in pediatric patients.
- The staged surgical approach highlights a viable strategy for treating severe spinal cord compression due to congenital deformities.
Abstract:
The case of a four-year-old child is described who presented to our institution with cervicothoracic deformity and a two-year history of progressive paraparesis. His past medical history was significant for meningocele which was closed at age two months. Imaging studies revealed severe congenital kyphosis with a hypoplastic T3 vertebra, as well as a tethered filum terminale with a conus lipoma. The spinal cord was found to be severely compressed at the apex of the kyphotic deformity. Discussion is focused on the diagnosis of tethered cord syndrome, and treatment options. In particular, this case required careful thought on the order of events, which followed initial tethered cord release and removal of the conus lipoma, and subsequent kyphectomy and fusion of the upper thoracic spine. A favorable clinical outcome was obtained with complete reversal of the paraparesis.
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