Paediatric laryngeal malignant nerve sheath tumour

Malignant nerve sheath tumours (MNSTs) are more frequently diagnosed in the extremities, the chest wall and the abdominal wall. Laryngeal MNST is an extremely rare occurrence, particularly in children. We treated a laryngeal recurrence of MNST in a 13-year-old boy with chemotherapy followed by horizontal supraglottic laryngectomy extended to left arytenoid and ipsilateral vocal fold and bilateral neck dissection. Four years later, hemithyroidectomy was performed for thyroid MNST recurrence. At present, 6 years after last intervention, the patient shows no evidence of recurrent disease.