When cilia go bad: cilia defects and ciliopathies

Manfred Fliegauf1, Thomas Benzing, Heymut Omran

  • 1Department of Paediatrics and Adolescent Medicine, University Hospital Freiburg, 79106 Freiburg, Germany.

Summary

Cilia, hair-like organelles on cell surfaces, are increasingly recognized as causes of human diseases. Defects in cilia structure and function lead to widespread disorders affecting multiple organ systems.

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